J 2014

Atypical form of arrhythmogenic cardiomyopathy

NOVOTNÝ, Petr, Roman PANOVSKÝ, Vera FEITOVA, Pavla BALCARKOVA, Ilga GROCHOVA et. al.

Basic information

Original name

Atypical form of arrhythmogenic cardiomyopathy

Name in Czech

Atypická forma arytmogenní kardiomyopatie

Authors

NOVOTNÝ, Petr (203 Czech Republic, belonging to the institution), Roman PANOVSKÝ (203 Czech Republic, belonging to the institution), Vera FEITOVA (203 Czech Republic), Pavla BALCARKOVA (203 Czech Republic), Ilga GROCHOVA (203 Czech Republic) and Vladimír KINCL (203 Czech Republic, belonging to the institution)

Edition

Cor et Vasa, Praha, Medical Tribune CZ, 2014, 0010-8650

Other information

Language

English

Type of outcome

Článek v odborném periodiku

Field of Study

30201 Cardiac and Cardiovascular systems

Country of publisher

Czech Republic

Confidentiality degree

není předmětem státního či obchodního tajemství

RIV identification code

RIV/00216224:14110/14:00087498

Organization unit

Faculty of Medicine

UT WoS

000409982000005

Keywords in English

Arrhythmogenic right ventricular dysplasia/cardiomyopathy; Cardiac magnetic resonance; Coronary angiography

Tags

Tags

Reviewed
Změněno: 18/5/2017 14:14, Ing. Mgr. Věra Pospíšilíková

Abstract

V originále

A case of a family suffering from arrhythmogenic cardiomyopathy affecting dominantly the left ventricle of the heart was diagnosed in our hospital. A forty-six-year-old man was admitted to the emergency room because of a collapse with both respiratory and circulatory arrest during a sport activity. Fibrillation of the ventricles was initially registered upon electrocardiography, and there had been several sudden deaths at a young age in the patient's family. There was no significant stenosis of his coronary arteries and because of the electrocardiographic and echocardiographic findings, cardiac magnetic resonance was indicated. The cardiac magnetic resonance finding on the patient's heart probably corresponds to a less frequent type of arrhythmogenic cardiomyopathy with dominant left ventricular involvement. The patient's first-degree relatives underwent comprehensive examinations at our cardiology department, and a similar cardiac magnetic resonance finding concerning the heart was made in the younger brother of the proband. Both brothers had an implantable cardioverter-defibrillator implanted and the whole family remains subject to regular follow-ups at our department.