Ebstein's anomaly with significant dysplasia of the tricuspid
valve presenting at 73 years of age. A case report

J 2019

Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report

KOC, Lumír, Jiri ONDRASEK, Tomas ZATOCIL, Anna NECASOVA, Jindřich ŠPINAR et. al.

Basic information

Original name

Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report

Authors

KOC, Lumír (203 Czech Republic, guarantor, belonging to the institution), Jiri ONDRASEK (203 Czech Republic), Tomas ZATOCIL (203 Czech Republic), Anna NECASOVA (203 Czech Republic) and Jindřich ŠPINAR (203 Czech Republic, belonging to the institution)

Edition

Cor et Vasa, AMSTERDAM, ELSEVIER SCIENCE BV, 2019, 0010-8650

Other information

Language

English

Type of outcome

Článek v odborném periodiku

Field of Study

30201 Cardiac and Cardiovascular systems

Country of publisher

Netherlands

Confidentiality degree

není předmětem státního či obchodního tajemství

References:

URL

RIV identification code

RIV/00216224:14110/19:00112953

Organization unit

Faculty of Medicine

DOI

http://dx.doi.org/10.1016/j.crvasa.2018.07.004

UT WoS

000472526800010

Keywords in English

Ebstein's anomaly; Tricuspid regurgitation; Tricuspid valve dysplasia; Tricuspid valve replacement

Abstract

V originále

Ebstein's anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient's problems.

Citovat

KOC, Lumír, Jiri ONDRASEK, Tomas ZATOCIL, Anna NECASOVA and Jindřich ŠPINAR. Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report. Cor et Vasa. AMSTERDAM: ELSEVIER SCIENCE BV, 2019, vol. 61, No 3, p. 314-317. ISSN 0010-8650. Available from: https://dx.doi.org/10.1016/j.crvasa.2018.07.004.

@article{1622877,
   author = {Koc, Lumír and Ondrasek, Jiri and Zatocil, Tomas and Necasova, Anna and Špinar, Jindřich},
   article_location = {AMSTERDAM},
   article_number = {3},
   doi = {http://dx.doi.org/10.1016/j.crvasa.2018.07.004},
   keywords = {Ebstein's anomaly; Tricuspid regurgitation; Tricuspid valve dysplasia; Tricuspid valve replacement},
   language = {eng},
   issn = {0010-8650},
   journal = {Cor et Vasa},
   title = {Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report},
   url = {http://dx.doi.org/10.1016/j.crvasa.2018.07.004},
   volume = {61},
   year = {2019}
}

TY  - JOUR
ID  - 1622877
AU  - Koc, Lumír - Ondrasek, Jiri - Zatocil, Tomas - Necasova, Anna - Špinar, Jindřich
PY  - 2019
TI  - Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report
JF  - Cor et Vasa
VL  - 61
IS  - 3
SP  - 314-317
EP  - 314-317
PB  - ELSEVIER SCIENCE BV
SN  - 00108650
KW  - Ebstein's anomaly
KW  - Tricuspid regurgitation
KW  - Tricuspid valve dysplasia
KW  - Tricuspid valve replacement
UR  - http://dx.doi.org/10.1016/j.crvasa.2018.07.004
L2  - http://dx.doi.org/10.1016/j.crvasa.2018.07.004
N2  - Ebstein's anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient's problems.
ER  -

KOC, Lumír, Jiri ONDRASEK, Tomas ZATOCIL, Anna NECASOVA and Jindřich ŠPINAR. Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report. \textit{Cor et Vasa}. AMSTERDAM: ELSEVIER SCIENCE BV, 2019, vol.~61, No~3, p.~314-317. ISSN~0010-8650. Available from: https://dx.doi.org/10.1016/j.crvasa.2018.07.004.

Detailed Information on Publication Record