KOC, Lumír, Jiri ONDRASEK, Tomas ZATOCIL, Anna NECASOVA and Jindřich ŠPINAR. Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report. Cor et Vasa. AMSTERDAM: ELSEVIER SCIENCE BV, 2019, vol. 61, No 3, p. 314-317. ISSN 0010-8650. Available from: https://dx.doi.org/10.1016/j.crvasa.2018.07.004.
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Basic information
Original name Ebstein's anomaly with significant dysplasia of the tricuspid valve presenting at 73 years of age. A case report
Authors KOC, Lumír (203 Czech Republic, guarantor, belonging to the institution), Jiri ONDRASEK (203 Czech Republic), Tomas ZATOCIL (203 Czech Republic), Anna NECASOVA (203 Czech Republic) and Jindřich ŠPINAR (203 Czech Republic, belonging to the institution).
Edition Cor et Vasa, AMSTERDAM, ELSEVIER SCIENCE BV, 2019, 0010-8650.
Other information
Original language English
Type of outcome Article in a journal
Field of Study 30201 Cardiac and Cardiovascular systems
Country of publisher Netherlands
Confidentiality degree is not subject to a state or trade secret
WWW URL
RIV identification code RIV/00216224:14110/19:00112953
Organization unit Faculty of Medicine
Doi http://dx.doi.org/10.1016/j.crvasa.2018.07.004
UT WoS 000472526800010
Keywords in English Ebstein's anomaly; Tricuspid regurgitation; Tricuspid valve dysplasia; Tricuspid valve replacement
Tags 14110211, rivok
Tags International impact, Reviewed
Changed by Changed by: Mgr. Tereza Miškechová, učo 341652. Changed: 11/5/2020 11:07.
Abstract
Ebstein's anomaly (EA) is a rare congenital heart defect, characterized by an anomalous tricuspid valve displaced towards the apex of the right ventricle (RV); it is usually accompanied by regurgitation. While its severe forms with an extremely dilated functional RV and oppression of the left heart chambers result in the development of severe heart failure at a young age and, in some cases, even prenatally, patients with mild EA may live until old age with the condition unrecognized. We present the case of a patient with a milder form of EA and a contribution of dysplasia, with the disease undiagnosed until his eighties when he developed heart failure accompanied by significant tricuspid regurgitation. Tricuspid valve replacement with a bioprosthesis and atrial septal defect occlusion were followed by significant improvement of RV function and remission of the patient's problems.
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