Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK)
Syndrome: A Case Report

J 2022

Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report

HUDEC, Jan and Martina KOSINOVÁ

Basic information

Original name

Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report

Authors

HUDEC, Jan (203 Czech Republic, belonging to the institution) and Martina KOSINOVÁ (203 Czech Republic, guarantor, belonging to the institution)

Edition

Children, Basel, MDPI, 2022, 2227-9067

Other information

Language

English

Type of outcome

Článek v odborném periodiku

Field of Study

30223 Anaesthesiology

Country of publisher

Switzerland

Confidentiality degree

není předmětem státního či obchodního tajemství

References:

Children

Impact factor

Impact factor: 2.400

RIV identification code

RIV/00216224:14110/22:00126747

Organization unit

Faculty of Medicine

DOI

http://dx.doi.org/10.3390/children9060869

UT WoS

000818364800001

Keywords in English

ZTTK syndrome; neuromuscular scoliosis; anesthesia; case report

Abstract

V originále

Zhu-Tokita-Takenouchi-Kim (ZTTK) syndrome is an extremely rare multiorgan disorder, first described in 2015. Nowadays, about 50 patients with ZTTK syndrome have been reported, but there are no data about management during anesthesia. ZTTK syndrome patients can be indicated for surgery of musculoskeletal deformations and corrections of cardiovascular or urogenital malformations. This syndrome can be challenging for the anesthetic team based on the clinical manifestation of the syndrome. Because there are no recommendations for the management of these patients, anesthesiologists have to study typical symptoms, anatomy and possible expected changes in pathophysiology in perioperative period. One of the most dreaded anesthetic complications, the scenario “can not intubate, can not ventilate” could occur in these patients. The goal of this publication is to show options for anesthetic and perioperative management of this new rare syndrome with no published studies about management and approach in the perioperative period. The anesthetic team should choose the safest available approach. We present the first case report of anesthesia of a patient with ZTTK syndrome, a 7-year-old boy indicated for posterior neuromuscular scoliosis correction and fusion. This case describes the author’s experiences with anesthetic management and mentions possible early postoperative complications. Adequate understanding of this syndrome can reduce perioperative complications and improve patient outcomes after surgery.

Links

MUNI/A/1178/2021, interní kód MU

Name: Simulační trénink v identifikaci a prevenci kritických událostí v anesteziologii a intenzivní medicíně III. (Acronym: SIMUCRITICAL)

Investor: Masaryk University

Citovat

HUDEC, Jan and Martina KOSINOVÁ. Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report. Children. Basel: MDPI, 2022, vol. 9, No 6, p. 1-6. ISSN 2227-9067. Available from: https://dx.doi.org/10.3390/children9060869.

@article{2219980,
   author = {Hudec, Jan and Kosinová, Martina},
   article_location = {Basel},
   article_number = {6},
   doi = {http://dx.doi.org/10.3390/children9060869},
   keywords = {ZTTK syndrome; neuromuscular scoliosis; anesthesia; case report},
   language = {eng},
   issn = {2227-9067},
   journal = {Children},
   title = {Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report},
   url = {https://www.mdpi.com/2227-9067/9/6/869},
   volume = {9},
   year = {2022}
}

TY  - JOUR
ID  - 2219980
AU  - Hudec, Jan - Kosinová, Martina
PY  - 2022
TI  - Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report
JF  - Children
VL  - 9
IS  - 6
SP  - 1-6
EP  - 1-6
PB  - MDPI
SN  - 22279067
KW  - ZTTK syndrome
KW  - neuromuscular scoliosis
KW  - anesthesia
KW  - case report
UR  - https://www.mdpi.com/2227-9067/9/6/869
N2  - Zhu-Tokita-Takenouchi-Kim (ZTTK) syndrome is an extremely rare multiorgan disorder, first described in 2015. Nowadays, about 50 patients with ZTTK syndrome have been reported, but there are no data about management during anesthesia. ZTTK syndrome patients can be indicated for surgery of musculoskeletal deformations and corrections of cardiovascular or urogenital malformations. This syndrome can be challenging for the anesthetic team based on the clinical manifestation of the syndrome. Because there are no recommendations for the management of these patients, anesthesiologists have to study typical symptoms, anatomy and possible expected changes in pathophysiology in perioperative period. One of the most dreaded anesthetic complications, the scenario “can not intubate, can not ventilate” could occur in these patients. The goal of this publication is to show options for anesthetic and perioperative management of this new rare syndrome with no published studies about management and approach in the perioperative period. The anesthetic team should choose the safest available approach. We present the first case report of anesthesia of a patient with ZTTK syndrome, a 7-year-old boy indicated for posterior neuromuscular scoliosis correction and fusion. This case describes the author’s experiences with anesthetic management and mentions possible early postoperative complications. Adequate understanding of this syndrome can reduce perioperative complications and improve patient outcomes after surgery.
ER  -

HUDEC, Jan and Martina KOSINOVÁ. Anesthesia of the Patient with Zhu-Tokita-Takenouchi-Kim (ZTTK) Syndrome: A Case Report. \textit{Children}. Basel: MDPI, 2022, vol.~9, No~6, p.~1-6. ISSN~2227-9067. Available from: https://dx.doi.org/10.3390/children9060869.

Detailed Information on Publication Record