FABIAN, I. D., A. W. STACEY, A. FOSTER, T. T. KIVELA, F. L. MUNIER, N. KEREN-FROIM, N. GOMEL, N. CASSOUX, M. S. SAGOO, M. AL REDDY, L. AL HARBY, M. ZONDERVAN, C. BASCARAN, E. ABDALLAH, S. U. ABDULLAHI, S. A. BOUBACAR, D. S. ADEMOLA-POPOOLA, A. ADIO, A. E. AGHAJI, S. A. PORTABELLA, A. I. A. BIO, A. M. ALI, D. B. ALIA, C. ALL-ERIKSSON, A. A. ALMEIDA, K. M. ALSAWIDI, R. ANTONINO, N. J. ASTBURY, R. ATSIAYA, J. BALAGUER, W. BALWIERZ, H. BARRANCO, M. B. POPOVIC, S. BENMILOUD, N. B. GUEBESSI, R. C. BERETE, S. J. BIDDULPH, E. M. BIEWALD, S. BLUM, N. BOBROVA, M. BOEHME, N. BORNFELD, G. C. BOUDA, H. BOUGUILA, A. BOUMEDANE, B. G. BRICHARD, I. M. CAPRA, G. CASTELA, J. CATALA-MORA, G. L. CHANTADA, V. S. CHERNODRINSKA, F. S. CHIWANGA, K. CIESLIK, C. COMSA, M. G. C. LLANO, M. CSOKA, I. V. DA GAMA, A. DAVIDSON, P. DE POTTER, L. DESJARDINS, M. D. DRAGOMIR, M. DU BRUYN, A. EL KETTANI, A. M. ELBAHI, D. ELGALALY, A. M. ELHADDAD, M. M. A. ELHASSAN, M. M. ELZEMBELY, V. A. ESSUMAN, T. G. A. EVINA, O. FASINA, A. FERNANDEZ-TEIJEIRO, M. GANDIWA, D. G. ALDANA, J. A. GEEL, Z. GIZACHEW, P. A. GREGERSEN, K. M. GUEDENON, T. HADJISTILIANOU, S. HASSAN, S. HEDEROVA, L. HESSISSEN, D. F. HORDOFA, M. HUMMLEN, K. HUSAKOVA, R. IDA, V. R. ILIC, H. JENKINSON, T. B. A. KABESHA, R. L. KABORE, A. KALINAKI, N. KAPELUSHNIK, T. KARDAVA, P. K. KEMILEV, Tomáš KEPÁK, Z. KHOTENASHVILI, A. KLETT, J. E. K. K. PALET, D. KRIVAITIENE, M. KRUGER, A. KYARA, E. S. LACHMANN, S. LATINOVIC, K. LECUONA, R. M. LUKAMBA, L. LUMBROSO, L. LYSYTSIA, E. MAKA, M. MAKAN, C. MANDA, N. M. BEGUE, I. O. MATENDE, M. MATUA, I. MAYET, F. B. MBUMBA, A. A. MENGESHA, E. MIDENA, F. G. MNDEME, A. A. MOHAMEDANI, A. C. MOLL, C. MOREIRA, M. S. MSINA, G. MSUKWA, K. I. MUMA, G. MURGOI, K. O. MUSA, H. MUSTAK, O. M. MUYEN, G. NAIDU, L. NAUMENKO, P. A. N. ROTH, V. NEROEV, M. NIKITOVIC, E. D. NKANGA, H. NKUMBE, M. NYAYWA, G. OBONO-OBIANG, N. C. OGUEGO, A. OLECHOWSKI, A. H. OSCAR, P. OSEI-BONSU, S. L. PAINTER, V. PAINTSIL, L. PAIVA, R. PAPYAN, R. PARROZZANI, M. PARULEKAR, K. PAWINSKA-WASIKOWSKA, S. PERIC, R. PHILBERT, P. POCHOP, V. G. POLYAKOV, M. T. POMPE, J. J. PONS, L. RAOBELA, L. A. RENNER, D. REYNDERS, D. RIBADU, M. M. RIHEIA, P. RITTER-SOVINZ, S. SAAKYAN, A. M. A. SAID, S. S. PACHECO, T. A. SCANLAN, J. SCHOEMAN, S. SEREGARD, S. T. SHERIEF, S. S. CHEIKH, S. SILVA, T. SOROCHYNSKA, G. SSALI, C. STATHOPOULOS, B. S. KRANJC, D. K. STONES, K. SVOJGR, F. SYLLA, G. TAMAMYAN, A. TANDILI, B. TATESHI, T. THEOPHILE, F. TRAORE, H. TYAU-TYAU, A. B. UMAR, S. F. URBAK, T. L. USHAKOVA, S. VALEINA, M. V. WIJSARD, N. V. VELEVA-KRASTEVA, M. VIKSNINS, W. WACKERNAGEL, K. WADDELL, P. D. WADE, A. H. W. NIGERIA, A. D. C. WIME, C. W. DOD, J. M. YANGA, V. A. YAROVAYA, A. A. YAROVOY, E. ZEIN, S. SHARABI, K. ZHILYAEVA, O. A. O. ZIKO and R. BOWMAN. Travel burden and clinical presentation of retinoblastoma: analysis of 1024 patients from 43 African countries and 518 patients from 40 European countries. The British journal of ophthalmology : incorporating the Royal London ophthalmic hospital reports, the Ophthalmic review and the Ophthalmoscope. London: British Journal of Ophthalmology, 2021, vol. 105, No 10, p. 1435-1443. ISSN 0007-1161. Available from: https://dx.doi.org/10.1136/bjophthalmol-2020-316613.
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Original name Travel burden and clinical presentation of retinoblastoma: analysis of 1024 patients from 43 African countries and 518 patients from 40 European countries
Authors FABIAN, I. D. (guarantor), A. W. STACEY, A. FOSTER, T. T. KIVELA, F. L. MUNIER, N. KEREN-FROIM, N. GOMEL, N. CASSOUX, M. S. SAGOO, M. AL REDDY, L. AL HARBY, M. ZONDERVAN, C. BASCARAN, E. ABDALLAH, S. U. ABDULLAHI, S. A. BOUBACAR, D. S. ADEMOLA-POPOOLA, A. ADIO, A. E. AGHAJI, S. A. PORTABELLA, A. I. A. BIO, A. M. ALI, D. B. ALIA, C. ALL-ERIKSSON, A. A. ALMEIDA, K. M. ALSAWIDI, R. ANTONINO, N. J. ASTBURY, R. ATSIAYA, J. BALAGUER, W. BALWIERZ, H. BARRANCO, M. B. POPOVIC, S. BENMILOUD, N. B. GUEBESSI, R. C. BERETE, S. J. BIDDULPH, E. M. BIEWALD, S. BLUM, N. BOBROVA, M. BOEHME, N. BORNFELD, G. C. BOUDA, H. BOUGUILA, A. BOUMEDANE, B. G. BRICHARD, I. M. CAPRA, G. CASTELA, J. CATALA-MORA, G. L. CHANTADA, V. S. CHERNODRINSKA, F. S. CHIWANGA, K. CIESLIK, C. COMSA, M. G. C. LLANO, M. CSOKA, I. V. DA GAMA, A. DAVIDSON, P. DE POTTER, L. DESJARDINS, M. D. DRAGOMIR, M. DU BRUYN, A. EL KETTANI, A. M. ELBAHI, D. ELGALALY, A. M. ELHADDAD, M. M. A. ELHASSAN, M. M. ELZEMBELY, V. A. ESSUMAN, T. G. A. EVINA, O. FASINA, A. FERNANDEZ-TEIJEIRO, M. GANDIWA, D. G. ALDANA, J. A. GEEL, Z. GIZACHEW, P. A. GREGERSEN, K. M. GUEDENON, T. HADJISTILIANOU, S. HASSAN, S. HEDEROVA, L. HESSISSEN, D. F. HORDOFA, M. HUMMLEN, K. HUSAKOVA, R. IDA, V. R. ILIC, H. JENKINSON, T. B. A. KABESHA, R. L. KABORE, A. KALINAKI, N. KAPELUSHNIK, T. KARDAVA, P. K. KEMILEV, Tomáš KEPÁK (203 Czech Republic, belonging to the institution), Z. KHOTENASHVILI, A. KLETT, J. E. K. K. PALET, D. KRIVAITIENE, M. KRUGER, A. KYARA, E. S. LACHMANN, S. LATINOVIC, K. LECUONA, R. M. LUKAMBA, L. LUMBROSO, L. LYSYTSIA, E. MAKA, M. MAKAN, C. MANDA, N. M. BEGUE, I. O. MATENDE, M. MATUA, I. MAYET, F. B. MBUMBA, A. A. MENGESHA, E. MIDENA, F. G. MNDEME, A. A. MOHAMEDANI, A. C. MOLL, C. MOREIRA, M. S. MSINA, G. MSUKWA, K. I. MUMA, G. MURGOI, K. O. MUSA, H. MUSTAK, O. M. MUYEN, G. NAIDU, L. NAUMENKO, P. A. N. ROTH, V. NEROEV, M. NIKITOVIC, E. D. NKANGA, H. NKUMBE, M. NYAYWA, G. OBONO-OBIANG, N. C. OGUEGO, A. OLECHOWSKI, A. H. OSCAR, P. OSEI-BONSU, S. L. PAINTER, V. PAINTSIL, L. PAIVA, R. PAPYAN, R. PARROZZANI, M. PARULEKAR, K. PAWINSKA-WASIKOWSKA, S. PERIC, R. PHILBERT, P. POCHOP, V. G. POLYAKOV, M. T. POMPE, J. J. PONS, L. RAOBELA, L. A. RENNER, D. REYNDERS, D. RIBADU, M. M. RIHEIA, P. RITTER-SOVINZ, S. SAAKYAN, A. M. A. SAID, S. S. PACHECO, T. A. SCANLAN, J. SCHOEMAN, S. SEREGARD, S. T. SHERIEF, S. S. CHEIKH, S. SILVA, T. SOROCHYNSKA, G. SSALI, C. STATHOPOULOS, B. S. KRANJC, D. K. STONES, K. SVOJGR, F. SYLLA, G. TAMAMYAN, A. TANDILI, B. TATESHI, T. THEOPHILE, F. TRAORE, H. TYAU-TYAU, A. B. UMAR, S. F. URBAK, T. L. USHAKOVA, S. VALEINA, M. V. WIJSARD, N. V. VELEVA-KRASTEVA, M. VIKSNINS, W. WACKERNAGEL, K. WADDELL, P. D. WADE, A. H. W. NIGERIA, A. D. C. WIME, C. W. DOD, J. M. YANGA, V. A. YAROVAYA, A. A. YAROVOY, E. ZEIN, S. SHARABI, K. ZHILYAEVA, O. A. O. ZIKO and R. BOWMAN.
Edition The British journal of ophthalmology : incorporating the Royal London ophthalmic hospital reports, the Ophthalmic review and the Ophthalmoscope, London, British Journal of Ophthalmology, 2021, 0007-1161.
Other information
Original language English
Type of outcome Article in a journal
Field of Study 30204 Oncology
Country of publisher United Kingdom of Great Britain and Northern Ireland
Confidentiality degree is not subject to a state or trade secret
WWW URL
Impact factor Impact factor: 5.908
RIV identification code RIV/00216224:14110/21:00124151
Organization unit Faculty of Medicine
Doi http://dx.doi.org/10.1136/bjophthalmol-2020-316613
UT WoS 000702446300022
Keywords in English Epidemiology; Neoplasia
Tags 14110321, rivok
Tags International impact, Reviewed
Changed by Changed by: Mgr. Tereza Miškechová, učo 341652. Changed: 15/2/2022 09:04.
Abstract
Background The travel distance from home to a treatment centre, which may impact the stage at diagnosis, has not been investigated for retinoblastoma, the most common childhood eye cancer. We aimed to investigate the travel burden and its impact on clinical presentation in a large sample of patients with retinoblastoma from Africa and Europe. Methods A cross-sectional analysis including 518 treatment-naive patients with retinoblastoma residing in 40 European countries and 1024 treatment-naive patients with retinoblastoma residing in 43 African countries. Results Capture rate was 42.2% of expected patients from Africa and 108.8% from Europe. African patients were older (95% CI -12.4 to -5.4, p<0.001), had fewer cases of familial retinoblastoma (95% CI 2.0 to 5.3, p<0.001) and presented with more advanced disease (95% CI 6.0 to 9.8, p<0.001); 43.4% and 15.4% of Africans had extraocular retinoblastoma and distant metastasis at the time of diagnosis, respectively, compared to 2.9% and 1.0% of the Europeans. To reach a retinoblastoma centre, European patients travelled 421.8 km compared to Africans who travelled 185.7 km (p<0.001). On regression analysis, lower-national income level, African residence and older age (p<0.001), but not travel distance (p=0.19), were risk factors for advanced disease. Conclusions Fewer than half the expected number of patients with retinoblastoma presented to African referral centres in 2017, suggesting poor awareness or other barriers to access. Despite the relatively shorter distance travelled by African patients, they presented with later-stage disease. Health education about retinoblastoma is needed for carers and health workers in Africa in order to increase capture rate and promote early referral.
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