JUŘÍKOVÁ, Lenka, Lucia MASÁROVÁ, Roman PANOVSKÝ, Martin PEŠL, Kamila ŽONDRA REVENDOVÁ, Ondřej VOLNÝ, Věra FEITOVÁ, Tomáš HOLEČEK, Vladimír KINCL, Pavlína DANHOFER, Stanislav VOHÁŇKA, Jana HABERLOVÁ a Podolská KAROLÍNA. Decreased quality of life in Duchenne muscular disease patients related to functional neurological and cardiac impairment. Frontiers in Neurology. LAUSANNE: FRONTIERS MEDIA SA, 2024, roč. 15, February 2024, s. 1-11. ISSN 1664-2295. Dostupné z: https://dx.doi.org/10.3389/fneur.2024.1360385. |
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@article{2374257, author = {Juříková, Lenka and Masárová, Lucia and Panovský, Roman and Pešl, Martin and Žondra Revendová, Kamila and Volný, Ondřej and Feitová, Věra and Holeček, Tomáš and Kincl, Vladimír and Danhofer, Pavlína and Voháňka, Stanislav and Haberlová, Jana and Karolína, Podolská}, article_location = {LAUSANNE}, article_number = {February 2024}, doi = {http://dx.doi.org/10.3389/fneur.2024.1360385}, keywords = {quality of life; Duchenne muscular dystrophy; cardiac magnetic resonance; neurological status; cardiac impairment}, language = {eng}, issn = {1664-2295}, journal = {Frontiers in Neurology}, title = {Decreased quality of life in Duchenne muscular disease patients related to functional neurological and cardiac impairment}, url = {https://www.frontiersin.org/journals/neurology/articles/10.3389/fneur.2024.1360385/full?utm_source=F-NTF&utm_medium=EMLX&utm_campaign=PRD_FEOPS_20170000_ARTICLE}, volume = {15}, year = {2024} }
TY - JOUR ID - 2374257 AU - Juříková, Lenka - Masárová, Lucia - Panovský, Roman - Pešl, Martin - Žondra Revendová, Kamila - Volný, Ondřej - Feitová, Věra - Holeček, Tomáš - Kincl, Vladimír - Danhofer, Pavlína - Voháňka, Stanislav - Haberlová, Jana - Karolína, Podolská PY - 2024 TI - Decreased quality of life in Duchenne muscular disease patients related to functional neurological and cardiac impairment JF - Frontiers in Neurology VL - 15 IS - February 2024 SP - 1-11 EP - 1-11 PB - FRONTIERS MEDIA SA SN - 16642295 KW - quality of life KW - Duchenne muscular dystrophy KW - cardiac magnetic resonance KW - neurological status KW - cardiac impairment UR - https://www.frontiersin.org/journals/neurology/articles/10.3389/fneur.2024.1360385/full?utm_source=F-NTF&utm_medium=EMLX&utm_campaign=PRD_FEOPS_20170000_ARTICLE N2 - In this prospective study involving 37 Duchenne muscular dystrophy (DMD) patients aged 8–18 years and older, we examined the impact of neurological and cardiac factors on quality of life (QoL). Our findings revealed a negative correlation between upper limb movement and overall mobility, self-service, and usual activities. Ambulatory and non-ambulatory DMD patients showed significant differences in mobility-related parameters. Cardiac evaluations demonstrated associations between mitral annular plane systolic excursion (MAPSE) and mobility-related aspects. The PEDSQL 3.0 neuromuscular model questionnaire further highlighted age-related and movement-related correlations with QoL. The loss of ambulatory status and reduced upper limb movement were negatively associated with QoL, while upper limb movement positively correlated with septal MAPSE. However, no significant associations were found between MAPSE and anxiety/depression. These findings underscore the multifaceted impact of DMD on QoL and emphasize the importance of considering both neurological and cardiac factors in comprehensive patient care. ER -
JUŘÍKOVÁ, Lenka, Lucia MASÁROVÁ, Roman PANOVSKÝ, Martin PEŠL, Kamila ŽONDRA REVENDOVÁ, Ondřej VOLNÝ, Věra FEITOVÁ, Tomáš HOLEČEK, Vladimír KINCL, Pavlína DANHOFER, Stanislav VOHÁŇKA, Jana HABERLOVÁ a Podolská KAROLÍNA. Decreased quality of life in Duchenne muscular disease patients related to functional neurological and cardiac impairment. \textit{Frontiers in Neurology}. LAUSANNE: FRONTIERS MEDIA SA, 2024, roč.~15, February 2024, s.~1-11. ISSN~1664-2295. Dostupné z: https://dx.doi.org/10.3389/fneur.2024.1360385.
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