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@inproceedings{568906, author = {Pokojová, Eva and Binková, Ilona and Merta, Zdeněk and Tomíšková, Marcela and Skřičková, Jana}, address = {Praha}, booktitle = {8th International Symposium for Cystic fibrosis}, keywords = {cystic fibrosis; pulmonary function evaluation; gene mutation}, language = {eng}, location = {Praha}, pages = {15-15}, publisher = {Karlova universita}, title = {Caring For Patients With Cystic Fibrosis: A three year experience}, year = {2005} }
TY - JOUR ID - 568906 AU - Pokojová, Eva - Binková, Ilona - Merta, Zdeněk - Tomíšková, Marcela - Skřičková, Jana PY - 2005 TI - Caring For Patients With Cystic Fibrosis: A three year experience PB - Karlova universita CY - Praha KW - cystic fibrosis KW - pulmonary function evaluation KW - gene mutation N2 - Fourteen patients aged 19 to 38 zears were followed up over 3 years. Genotype/phenotype correlations were made. Severizy of airway and gastrointerstinal disease was assessed. Relationship between the airway colonization and severity of airway disease was explored. The severity of CFRT gene mutation did not determine whether the diagnosis was made early or late, but insufficient pancreatic secretion was found in all pts. with severe mutation. A need for interdisciplinary approach is stressed. ER -
POKOJOVÁ, Eva, Ilona BINKOVÁ, Zdeněk MERTA, Marcela TOMÍŠKOVÁ a Jana SKŘIČKOVÁ. Caring For Patients With Cystic Fibrosis: A three year experience. In \textit{8th International Symposium for Cystic fibrosis}. Praha: Karlova universita, 2005, s.~15.
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